Vulvar lymphangioma circumscriptum: comparison of primary and acquired forms in a cohort of 57 patients.

Lymphoedema, a rare debilitating disorder usually involving limbs. For lymphoedema involving the genitalia, its terminology remains imprecise and not consensual. We kept the more appropriate classification, that is primary or acquired vulvar lymphangioma circumscriptum (VLC), as suggested by Vlastos et al. VLC is a very rare disease, causing major discomfort, aesthetic prejudice and risk of infection.

We included all women with VLC referred to our centre specialized in lymphology from January 1990 to April 2017; eight of them were previously published. We recorded the following characteristics: age at the first consultation, age at lymphoedema-symptom onset, symptom-onset-to-first-consultation interval, previous cancer, associated lower limb localization, previous cellulitis (erysipelas), body mass index, localized complications. These data allowed to make a comparative analysis between the primary and acquired VLC form. (J Eur Acad dermatol Venereol. 2018 Feb;32(2):e56-e58)